Eureka! Institutional Repository

Cystic Fibrosis is one of the most frequent hereditary diseases in the Caucasian population and also one of the most common causes of death during childhood. It is a polysystematic disease that is phenotypically characterized by disfunction of exocrine glands with main clinical manifestations from the respiratory, the digestive and the genital system and also from the sweat glands. These main manifestations are due to disturbance in transmembrane movement of Na + and Cl ions and as a result this creates sticky mucus that leads to obstructive pulmonary disease and dysfunction of the pancreas and the sweat glands. The aim of this work is to highlight the importance of respiratory physiotherapy in the daily lives of fibrous children. The contribution of respiratory physiotherapy is great as it helps the patient to cope with the demands of everyday life. We will refer to the disease ,pathophysiology, causes, suppression and the clinical picture of cystic fibrosis. The diagnosis of the disease is mainly done by the "sweat test". The prognosis is not encouraging, however, it has increased the average life expectancy and physiotherapy. Still we will refer to the daily routine of the patients and especially to their role physiotherapist in children with cystic fibrosis.